Exostoses,Multiple Hereditary
《英文msh詞典》Exostoses,Multiple Hereditary
[主題詞] Exostoses,Multiple Hereditary
[同義詞] Chondrodysplasia,Hereditary Deforming
[同義詞] Diaphyseal Aclasis
[同義詞] Exostoses,Familial
[同義詞] Exostoses,Hereditary Multiple
[同義詞] Exostoses,Multiple
[同義詞] Exostoses,Multiple Cartilaginous
[同義詞] Hereditary Multiple Exostoses
[同義詞] Osteochondromas,Multiple
[入口詞] Exostosis,Familial
[入口詞] Exostosis,Hereditary Multiple
[入口詞] Exostosis,Multiple
[入口詞] Exostosis,Multiple Cartilaginous
[入口詞] Hereditary Multiple Exostosis
[入口詞] Aclases,Diaphyseal
[入口詞] Aclasis,Diaphyseal
[入口詞] Cartilaginous Exostoses,Multiple
[入口詞] Cartilaginous Exostosis,Multiple
[入口詞] Chondrodysplasias,Hereditary Deforming
[入口詞] Deforming Chondrodysplasia,Hereditary
[入口詞] Deforming Chondrodysplasias,Hereditary
[入口詞] Diaphyseal Aclases
[入口詞] Familial Exostoses
[入口詞] Familial Exostosis
[入口詞] Hereditary Deforming Chondrodysplasia
[入口詞] Hereditary Deforming Chondrodysplasias
[入口詞] Hereditary Exostoses,Multiple
[入口詞] Multiple Cartilaginous Exostoses
[入口詞] Multiple Cartilaginous Exostosis
[入口詞] Multiple Exostoses
[入口詞] Multiple Exostoses,Hereditary
[入口詞] Multiple Exostosis
[入口詞] Multiple Exostosis,Hereditary
[入口詞] Multiple Hereditary Exostoses
[入口詞] Multiple Osteochondroma
[入口詞] Multiple Osteochondromas
[入口詞] Osteochondroma,Multiple
[中文釋義] 外生骨疣,多發性遺傳性
[英文釋義] Hereditary disorder transmitted by an autosomal dominant gene and characterized by multiple exostoses (multiple osteochondromas) near the ends of long bones. The genetic abnormality results in a defect in the osteoclastic activity at the metaphyseal ends of the bone during the remodeling process in childhood or early adolescence. The metaphyses develop benign,bony outgrowths often capped by cartilage. A small number undergo neoplastic transformation.